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"At that time following a biopsy she was diagnosed as having pineoblastoma.
(b) that the cause of death was recurrent pineoblastoma.
Pineoblastoma may occur in patients with hereditary uni- or bilateral retinoblastoma.
When retinoblastoma patients present with pineoblastoma this is characterized as "trilateral retinoblastoma".
A pineoblastoma is a supratentorial midline primitive neuroectodermal tumor.
In most cases trilateral retinoblastoma presents itself as pineoblastoma (pineal TRb).
Maya, of Romford, Essex, England, was first diagnosed with pineoblastoma in September 2006 and doctors gave her a 50 percent survival rate.
In addition, inherited uni- or bilateral retinoblastomas may be associated with pineoblastoma and other malignant midline supratentorial primitive neuroectodermal tumors (PNET) with a dismal outcome; retinoblastoma concurrent with a PNET is known as trilateral retinoblastoma.
Pineoblastoma (grade IV): A pineoblastoma is a rare tumor that is very likely to spread.